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OPA1

OPA,即視神經萎縮蛋白1,別名OpticAtrophyType1。它是由人類OPA1基因編碼的蛋白,主要在線粒體內膜上發揮作用。OPA1的作用機制包括調控線粒體的融合過程,維持線粒體形態和功能,以及參與線粒體呼吸鏈超級復合物的組裝和線粒體嵴的重塑。OPA1對維持細胞能量代謝、細胞死亡、增殖以及基因表達調控具有重要作用。OPA1的異常與多種疾病相關,尤其是與視神經萎縮(ADOA)和更廣泛的神經系統癥狀。

熱銷產品

OPA1 Antibody (CSB-PA016340LA01HU)

驗證數據

CSB-PA016340LA01HU

Western Blot
Positive WB detected in: Hela whole cell lysate, MCF-7 whole cell lysate, HepG2 whole cell lysate, K562 whole cell lysate, Mouse heart tissue
All lanes: OPA1 antibody at 1:2000
Secondary
Goat polyclonal to rabbit IgG at 1/50000 dilution
Predicted band size: 112, 116 kDa
Observed band size: 112 kDa

OPA1 Antibodies

OPA1 for Homo sapiens (Human)

OPA1 Proteins

OPA1 Proteins for Homo sapiens (Human)



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